摘要: |
免疫球蛋白(immunoglobulin,Ig)G4相关性疾病是近年来才被认识并得到广泛关注的一种系统性疾病,其以病变部位肿胀,受累组织大量淋巴浆细胞特别是IgG4阳性浆细胞浸润,席纹状纤维化为特点,或伴血清IgG4增高。目前研究发现IgG4相关性疾病可累及各个器官,例如胰腺(自发性胰腺炎)[1]、泪腺(米库利兹病)[2]、腹膜后(腹膜后纤维化)[3]、主动脉(主动脉瘤、主动脉炎)[4-5]、心脏(缩窄性心包炎)[6],及冠状动脉周假瘤[7]等。 |
关键词: 一例IgG4相关硬化性疾病 、心脏移植、护理 |
DOI: |
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基金项目:无 |
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PANCHUNFENG, shenjun, qinwei, WANGYING, suwei, wubojie
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ZHONGSHANHOSPITAL
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Abstract: |
Immunoglodbulin (Ig) G4-associated disease is a systemic disease that has recently been recognized and received extensive attention. It is characterized by swelling at the lesion site, infiltration of large numbers of lymphocytes, especially IGG4-positive plasma cells, and mat fibrosis, often accompanied by elevated serum IgG4, but can also be normal.Current research has found that IGG4-related diseases can affect various organs, such as the pancreas (spontaneous pancreatitis).[1]Lacrimal glands (Mikulitz's disease)[2]Retroperitoneal fibrosis[3]Aorta (aortic aneurysm, aortitis)[4-5]Heart (constrictive pericarditis)[6], and pericoronary pseudotumor[7]And so on. At present, the epidemiological data of IgG4-related cardiovascular diseases are scarce, and no relative articles have been reported in China. |
Key words: 无 |