摘要: |
嗜血细胞综合征,又称噬血细胞淋巴组织细胞增多症(HLH)是一组异质性疾病,其特征是由于T细胞、巨噬细胞和组织细胞的激活失控导致的高炎症状态,并伴有细胞因子的过度产生,除非及时发现和治疗,否则这种少见的疾病几乎是致命的。HLH是成人最严重的临床疾病之一,死亡率为40%,妊娠合并HLH的相关报道较少。本篇文章和大家分享1例妊娠继发HLH的病例,并作相关HLH的文献复习。 |
关键词: 妊娠 嗜血细胞综合征 |
DOI:10.12025/j.issn.1008-6358.2021.20200097 |
分类号:R714.25 |
基金项目:上海市科学技术委员会基金(17411966200). |
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A case of hematophilia syndrome secondary to pregnancy and review of literature |
sunhanxiang1, Ye Wei-ping2, gaoyuping1
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1.Xinhua Hospital, Affiliated to the School of Medicine, Shanghai Jiaotong University;2.Department of Obstetrics and Gynecology,Xinhua hospital,Medical College of Shanghai Jiaotong University
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Abstract: |
Hemophilic Syndrome, also known as hemophagocytosis (HLH), is a heterogeneous group of diseases characterized by a high state of inflammation due to uncontrolled activation of t cells, macrophages, and tissue cells, accompanied by overproduction of cytokines. this rare disease is almost fatal unless found and treated in time. HLH is one of the most serious clinical diseases in adults, with a mortality rate of 40% and fewer related reports of pregnancy with LH. This article is to share with you a case of pregnancy secondary LH and review the literature of relevant HLH. |
Key words: Pregnancy Hemophilic Syndrome |