Research progress of nutritional management of children with spinal muscular atrophy |
Received:June 15, 2020 Revised:October 09, 2020 Click here to download the full text |
Citation of this paper:GONG Xiao-yan,LU Zhong-ying,LI Wen-hui,ZHU Xiao-mei,HU Chao-ping,ZHOU Shui-zhen,LI Xi-hua,QIAN Tian,WANG Yi.Research progress of nutritional management of children with spinal muscular atrophy[J].Chinese Journal of Clinical Medicine,2021,28(4):699-704 |
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Author Name | Affiliation | E-mail | GONG Xiao-yan | Department of Clinical Nutrition, Children's Hospital, Fudan University, Shanghai 201102, China | | LU Zhong-ying | Department of Clinical Nutrition, Children's Hospital, Fudan University, Shanghai 201102, China | | LI Wen-hui | Department of Neurology, Children's Hospital, Fudan University, Shanghai 201102, China | | ZHU Xiao-mei | Department of Neurology, Children's Hospital, Fudan University, Shanghai 201102, China | | HU Chao-ping | Department of Neurology, Children's Hospital, Fudan University, Shanghai 201102, China | | ZHOU Shui-zhen | Department of Neurology, Children's Hospital, Fudan University, Shanghai 201102, China | | LI Xi-hua | Department of Neurology, Children's Hospital, Fudan University, Shanghai 201102, China | | QIAN Tian | Department of Clinical Nutrition, Children's Hospital, Fudan University, Shanghai 201102, China | | WANG Yi | Department of Neurology, Children's Hospital, Fudan University, Shanghai 201102, China | yiwang@shmu.edu.cn |
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Abstract:Spinal muscular atrophy (SMA) is a rare hereditary neuromuscular disease. Clinical manifestations of SMA include proximal limbs symmetrical and progressive muscle weakness and atrophy. Children with SMA are susceptible to swallowing dysfunction, gastrointestinal dysfunction, feeding difficulties, abnormal bone metabolism, and undernutrition/overnutrition. Currently, there is no standardized SMA nutrition support guideline. Patients need regular evaluations of growth and nutritional status. Nutritional interventions and treatments need to be done by professional dietitians. Individualized nutrition management plays an important role in improving the quality of life, delaying the illness, and prolonging the survival time of children with SMA. |
keywords:spinal muscular atrophy children nutrition management |
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